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este documento describe un amplio campo de anomalías embriológicas que afectan el aparato digestivo, se encontrarán muchas imágenes didácticas e información de cada una de las anomalías
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7/18/2019 Seminario Digestivo
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UNIVERSIDAD CENTRAL DEL ECUADOR FACULTAD DE CIENCIAS MÉDICAS
CARRERA DE MEDICINACÁTEDRA DE EMBRIOLOGÍA
SEMINARIO Nº2
ANOMALÍAS DE CAVIDADES CORPORALES Y APARATO DIGESTIVO
SEGUNDO SEMESTRE
PRIMER HEMICICLO
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ANOMALÍAS DE
CAVIDADES
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DEFECTOS PERICÁRDICOSCONGÉNITOS
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SIGNOS YSÍNTOMAS
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FORMACIÓN DEL DIAFRAGMA
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HERNIA DIAFRAGMÁTICACONGÉNITA O DE BOCHDALEK
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SIGNOS Y
SÌNTOMAS
DIAGNÓSTICO
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EVENTRACIÓN DEL DIAFRAGMA
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TRATAMIENTO
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GASTROSQUISIS Y HERNIAEPIGÁSTRICA CONGÉNITA
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TRATAMIENTO
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HERNIA HIATAL CONGÉNITA:
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Co!"#$"#%&!: C$&'(o! '" "!o)&*%+%! , &#o(+&-%"+o '"."!/)&*o
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HERNIA RETROESTERNAL OPARAESTERNAL DEL MORGAGNI
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EPIDEMIOLOGÍA
Constituye entre un 2 y un! "e to"#s $#s %erni#s
"i#&r#'()ti*#s
En $#s +erson#s #"u$t#sre+resent# un 2,! "e $#s%erni#s "i#&r#'()ti*#s
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DIAFRAGMA ACCESORIO
Se sit-# en $# *isur#o.$i*u#/ se+#r#n"o e$
$0.u$o in&erior "e$ resto "e$
+u$(0n "ere*%o/ &i1#"# +orsu +#rte intern# #$
+eri*#r"io y # $# +#re"tor)*i*# +or su +#rte
etern#3
He(it0r# "ere*%o/"i4i"i"o en "os
*o(+#rti(ientos/
+or un# (e(.r#n#(us*u$oten"inos#/
+#re*i"# #$"i#&r#'(#3
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5or(#*i0n "e$ "i#&r#'(#
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PENTALOGÍA DE CANTRELL
Co(.in#*i0n "e "e&e*tos6• 5isur# "e$ estern0n• E*t0+i# *#r"7#*#• On&#$o*e$e• Herni# "i#&r)'(#ti*# 8+or*i0n
#nterior9
• C#r"io+#t7#s *on':nit#s8*o(uni*#*i0n inter4entri*u$#r/tetr#$o'7# "e 5#$$ot93
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ANOMALÍAS DEL APARATODIGESTIVO
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ATRESIA ESOFÁGICA
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Atresi# y &7stu$# tr#;ueoeso&)'i*#3 A0 Atresi# eso&)'i*# *on &7stu$#Eiste #ire #."o(in#$3 B0 Atresi# eso&)'i*# sin &7stu$#Ausen*i# "e '#s #."o(in#$3 C0 57stu$# tr#;ueoeso&)'i*# sin #tresi#t<tr);ue#= e<es0&#'o
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ESTENOSIS ESOFÁGICA
T#(.i:n +ue"e "e.erse #$# &#$t# "e "es#rro$$o "e4#sos s#n'u7neos en $#
>on# #&e*t#"#/ o #%i+ertro&i# "e $#
su.(u*os# / "e $# *#+#(us*u$#r# etern# o "e
#(.#s
O*$usi0n +#r*i#$ "e $#$u> eso&)'i*#/ en e$ter*io "ist#$/ *o(o
*onse*uen*i# # un#re*#n#$i>#*i0nin*o(+$et# "e$ es0&#'o
"ur#nte $# o*t#4#se(#n#
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V%!%/ E'o!#/1%#& '" E!+"o!%!
E!o)*%#&
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ESÓFAGO CORTO
E$ es0&#'o no se#$#r'# $o
su&i*iente #(e"i"# ;ue*re*e e$ *ue$$o ye$ t0r#/
+ro"u*i:n"ose e$"es+$#>#(iento"e$ est0(#'o #tr#4:s "e$ %i#toeso&)'i*o
L# (#yor7# "e%erni#s
#+#re*en en $#e"#" #"u$t#
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ESTENOSIS HIPERTRÓFICA PILÓRICACONGÉNITA
O*$usi0n +#r*i#$ "e$# $u> +i$0ri*#/#&e*t# # ?@?!
4#rones y ?@B!(u1eres3 Se+resent# *o(o unen'ros#(iento "e$
+7$oro
Hi+ertro&i# "e $#*#+# (us*u$#r
*ir*u$#r y en (enor
'r#"o "e $# *#+#$on'itu"in#$ "e$est0(#'o # ni4e$
"e$ +7$oro3
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Te1i"o ')stri*o est0+i*o3 85oto to(#"# "e $# E(.rio$o'7#"e C#r$son9
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ATRESIA DUODENAL
• Oclusión luz
duodeno• Relacionado con
síndrome deDown
• Administran
líquidos vía
intravenosa.
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ESTENOSIS DUODENAL
• Oclusión parcial
duodeno
• Tratamientoquirurgico
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ANOMALIAS HEPATICAS
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ATRESIA BILIAR E3TRAHEPÁTICA
Falta de
recanalizacion de los
conductos biliares
hepatoportoenterostomía (técnica de
Kasai)
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TE4IDO PANCREATICO ACCESORIO
• ared del estomago e
duodeno• !igran c"lulas
pancre#ticas
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PANCREAS ANULAR • $anda plana %
delgada de te&ido
pancre#tico• Tratamiento
quir'rgico
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ENFERMEDAD FIBROQUÍSTICA DEL PÁNCREAS
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BA5O ACCESORIO• (na o varias masas
espl"cnias
peque)as.• !ide *cm de
di#metro• uede encontrarse
en el ligamento
gastroespl"cnico
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ATRESIAS Y ESTENOSIS DEL INTESTINO
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ATRESIAS Y ESTENOSIS DEL INTESTINODELGADO
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ATRESIA EN CÁSCARA DE MAN5ANA
• *+, de atresias.• orción pro-imal del %e%uno• i)os con ba&o peso % poca irrigación
de la arteria mesent"rica superior
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É
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ONFALOCELE CONGÉNITO
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HERNIA UMBILICAL
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FALTA DE ROTACIÓN INTESTINAL O
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FALTA DE ROTACIÓN INTESTINAL OCOLON DEL LADO I5QUIERDO
ROTACIÓN MI3TA Y VOLVULO
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ROTACIÓN MI3TA Y VOLVULO
ROTACIÓN INVERSA
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ROTACIÓN INVERSA
CIEGO Y APÉNDICE
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CIEGO Y APÉNDICESUBHEPÁTICOS
CIEGO MÓVIL
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CIEGO MÓVIL
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HERNIA INTERNA
Po*o &re*uenteIntestino "e$'#"ointro"u*i"o en e$
(esenterio "e$ #s# "e$intestino (e"io
5or(#*i0n "e un s#*o+#re*i"o # un# %er*i#
Asinto()ti*o
Dete*t#.$e en #uto+si#s
VÓLVULO DEL INTESTINO
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Torsi0n "e un se'(ento "e$intestino 8re'i0n "uo"eno yeyun#$9
Anor(#$ in'reso y &i1#i0n "e$
intestino en $# *#4i"#" #."o(in#$3 L# #rteri# y $# 4en# (es:nteri*#
su+eriores se enros*#n en e$ t#$$o y*#us#n o.stru**i0n3
C#us# '#n'ren#
MEDIO
DIVERTICULO DEL ILEON
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O DE MECKEL
o Ano(#$7# (uy *o(-n3o Re(#nente "e $# +or*i0n +roi(#$ "e$ s#*o 4ite$inoo 2 #$ 3 &re*eunte en ♂o E4#'in#*i0n en e$ .or"e #nti(esent:ri*o "e$ 7$eon # ! *(
"e $# unio i$eo*e*#$3 8o$s# +#re*i"# # un "e"o93o E$ "i4erti*u$o +ue"e est#r *one*t#"o #$ o(.$i'o3o Sinto(#s si(i$#res # un# #+en"ei*itis3
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Ó
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DUPLICACIÓN DEL TUBO
DIGESTIVOM#yor(ente #no(#$i#s;u7sit*#s o tu.u$#res #&e*t#n# *u#$;uier +#rte "e$ tu.o3Du+$i*#*iones ;uisti*#s ()s*o(unes3
L#s "u+$i*#*iones tu.u$#resse *o(uni*#n *on $# $u>intestin#$3C#us#s3, Re*#n#$i>#*i0n"e&e*tuos#/ &#$t# "et#.i*#(iento nor(#$3
A+#ri*i0n te(+r#n# "e $ossinto(#s3
ANOMALIAS DEL
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ANOMALIAS DELINTESTINO CAUDAL
DESARROLLONORMAL
L# (#yori# se $o*#$i># #ni4e$ "e $# re'ion
#norre*t#$/ se "e.e # un"es#rro$$o 4i4i#"o "e$t#.i;ue rorre*t#$
Se "i4i"en en #$t#s y .#1#sse'-n su ter(in#*i0n "e$*on"u*to #n#$3
MEGACOLON AGANGLIONAR CONGÉTINO O
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M G CO ON G NG ON CONG NO OENFERMEDAD DE HIRSCHSFRUNG
Di$#t#*i0n "e un se'(ento "e$ *o$on3 Pro"u*to "e $# #*u(u$#*i0n "e %e*es &e*#$es35re*ente en ♂
Ausen*i# "e ":$u$#s '#n'$ion#res +#r#si(+)ti*#s 8&#$t# "e (i'r#*i0n "e $#s *:$u$#s "e $#*rest# neur#$ entre $# !t# y B(# se(#n#93Ausen*i# "e +erist#$tis(o # ni4e$ "e$ se'(ento #'#n'$ion#r3En&er(e"#" (u$ti':i*# %ere"it#ri#Aso*i#"# *$ini*#(ente *on "istensi0n #."o(in#$3In*#+#*i"#" "e$ tr#nsito "e (e*onio3
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ATRESIA RECTAL
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Malformaciones anorrectales comunes: a) atresia rectal alta;b) atresia rectoanal baja; c) atresia rectal con ano patente;
d) estrenosis anal; e) fístula rectovesical
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ANORMAL NORMAL
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S" "!+%-& 6$" .& &+("!%&
&&. o#$((" " 7 '" #&'&80999 &#%'o! %o!0 E!1$"! $ '")"#+o '".&#%-%"+o (".&+%&-"+")("#$"+"
S% "! ;&<& o &.+& , !%"=%!+" o+(&!1&+o.o*>&! '"&#%-%"+o &!o#%&'&!o o0
!A"E #
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TRATAMIENTO
!A"E #
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Prolapso de una colostomía Estacomplicacin tiene tam!ién un
componente iatro"énico#
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!A"E $
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ATRESIA MEMBRANOSA O ANO
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IMPERFORADO
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AGENESIA ANORRECTAL
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AGENESIA ANORRECTAL
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AGENESIA ANORRECTAL CON 5FSTULARECTOAGINAL
AGENESIA ANORRECTAL CON 5FSTULARECTOURETRAL
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ESTENOSIS ANAL